Dysferlin Antibody (clone Ham3/17B2)

貨號 Cat. No.
VP-D504
規格 Size
1 ml
品牌 Brand
VECTOR Labs

Description

Mouse monoclonal antibody suitable for immunohistochemistry.



Functional Aspects:

Dysferlin is found in normal muscle but expression is reduced or lost in individuals with limb-girdle muscular dystrophy type 2B (LGMD2B) and Miyoshi myopathy (MM). Clone HAM3/17B2 was raised against a peptide from exons 11 and 12 of dysferlin. Clone Ham1/7B6 was raised against a peptide from exon 53.

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